Medical Isotopes, Inc. is a premier manufacturer of stable isotope chemicals labeled with: Deuterium, C13, N15, O18 and metal isotopes.  We specialize in custom synthesis with isotopes and non-labeled compounds.  
 
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Standards Used for Inborn Errors


Standards for Inborn Errors


Catalog Number Product Name Enrichment

Quantity

Price

Availability
 
Acryloyl glycine
5 mg $790 In Stock
 
Butyroyl carnitine
5 mg $820 In Stock
 
Butyroyl glycine
5 mg $790 In Stock
 
Butyroyl N-(methyl-d3)-carnitine
98%D
5 mg $1200
 
Acetyl carnitine
5 mg $790 In Stock
 
Crotonyl glycine
5 mg $790 In Stock
 
2,4-Decadienoic Acid
5 mg $790
 
Decanoyl carnitine
5 mg $1200 In Stock
 
Decanoyl N-(methyl-d3)3-carnitine
98%D
5 mg $1200
 
cis-4-Decenoic acid
5 mg $1500 In Stock
 
2-Decenoyl carnitine
5 mg $850
 
cis-4-Decenoyl carnitine
5 mg $900 In Stock
 
2-Decenoyl N-(methyl-d3)-carnitine
98%D
5 mg $1500
 
cis-4-Decenoyl N-(methyl-d3)-carnitine
98%D
5 mg $1500
 
Deuterated Desmosine
See below
1 mg $1975 In Stock
 
Ethyl trans-4-decenoate
5 g $990 In Stock
 
3-Hydroxy-2-ethylpropionic acid
5 mg $1500 In Stock
 
Furan-2,5-dicarboxylic Acid
5 mg $1200 In Stock
 
2-Furoyl glycine
5 mg $790 In Stock
 
Glutaroyl N-(methyl-d3)-carnitine
98%D
Inquire
 
Glutarylcarnitine
5 mg $1400 In stock
 
Heptanoyl glycine
Inquire
 
Hexanoyl carnitine
5 mg $850 In Stock
 
Hexanoyl glycine
5 mg $990 In Stock
 
Hexanoyl N-(methyl-d3)-carnitine
98%D
5 mg $1900
 
Homovanillic Acid
5 mg $1500 In Stock
 
2-Hydroxyadipic Acid
5 mg $990
 
4-Hydroxycyclohexylacetic acid
5 mg $1300 In Stock
 
3-Hydroxydodecandioic Acid
5 mg $1500 In Stock
 
3-Hydroxydodecanoic acid
5 mg $1100 In Stock
 
2-Hydroxyglutaric Acid
5 mg $1300 In Stock
 
3-Hydroxyglutaric Acid
5 mg $890 In Stock
 
5-Hydroxyhexanoic Acid
5 mg $990 In Stock
 
3-Hydroxyisobutyric Acid
1 mg $495 In Stock
5 mg $990 In Stock
 
3-Hydroxyisovaleric Acid
5 mg $790 In Stock
 
4-Hydroxyisovaleric Acid
5 mg $990 In Stock
 
Hydroxyisovaleroyl Carnitine
5 mg $1200
 
Hydroxyisovaleroyl N-(methyl-d3)-carnitine
98%D
5 mg $1600
 
7-Hydroxyoctanoic acid
5 mg $1500 In Stock
 
3-(3-Hydroxyphenyl)-3-hydroxypropionic Acid
5 mg $1050
 
4-Hydroxyphenylacetyl glycine
5 mg $1500
 
2-Hydroxyphytanic Acid
1 mg Inquire
 
3-Hydroxypropionic Acid
5 mg $790 In Stock
 
2-Hydroxysebacic Acid
5 mg $2500
 
3-Hydroxysebacic Acid
5 mg $1500 In Stock
 
3-Hydroxysuberic Acid
5 mg $990 In Stock
 
3-Hydroxytetradecanedioic acid
5 mg $2500
 
Isobutyroyl glycine
5 mg $790 In Stock
 
Isobutyroyl N-(methyl-d3)-Carnitine
98%D
5 mg $1800
 
Isobutyryl Carnitine
5 mg $950
 
Isovaleric Acid
1 g $550 In Stock
 
Isovaleroyl Carnitine
5 mg $960 In Stock
 
Isovaleroyl glycine
5 mg $790 In Stock
 
Isovaleroyl N-(methyl-d3)-Carnitine
98%D
5 mg $1600
 
Metacryloyl glycine
5 mg $790
 
Acetyl N-( methyl-d3)-carnitine
98%D
5 mg $1200
 
2-Methylacetoacetic acid
5 mg $990 In Stock
 
2-Methylbutyroyl Carnitine
5 mg $960 In Stock
 
2-Methylbutyroyl glycine
5 mg $990 In Stock
 
2-Methylbutyroyl N-(methyl-d3)-Carnitine
98%D
5 mg $1800
 
3-Methylcrotonyl Glycine
5 mg $790 In Stock
 
2-Methylglutaconic acid
5 mg $1200
 
3-Methylglutaconic acid
5 mg $790
 
2-Methylmalonoyl carnitine
5 mg $960
 
2-Methylmalonoyl N-(methyl-d3)-carnitine
98%D
5 mg $2200
 
3-Hydroxy-2-methylvaleric Acid
5 mg $790 In Stock
 
2-Methylvaleroyl glycine
5 mg $790 In Stock
 
Mirystoyl Carnitine
5 mg $960
 
Mirystoyl N-(methyl-d3)-carnitine
98%D
5 mg $1500
 
DL-Octanoyl carnitine
1 mg $1400 In Stock
5 mg $2500 In Stock
 
Octanoyl N-(methyl-d3)-carnitine
98%D
5 mg $1500
 
2-Octene-1,8-dioic Acid
5 mg $1300 In Stock
 
2-Oxoadipic Acid
5 mg $1350
 
3-Oxopentanoic Acid
5 mg $950 In Stock
 
2-Oxophytanic Acid
1 mg Inquire
 
Phenylacetyl glycine
5 mg $790
 
3-Hydroxy-3-phenylpropionic acid
5 mg $790 In Stock
 
3-Phenylpropionyl glycine
5 mg $1500 In Stock
 
cis-5-Tetradecenoic Acid
5 mg $1900 In Stock
 
Tiglyl glycine
5 mg $950 In Stock
 
Valeroyl glycine
5 mg $1500 In Stock

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