Inquire About a Product| Product: | 3-Hydroxyisovaleric Acid | ||||||||
|---|---|---|---|---|---|---|---|---|---|
| Catalog Number: | 5178 | ||||||||
| CAS Number: | 625-08-1 | ||||||||
| Synonyms: |
β-Hydroxy β-methylbutyric acid; HMB |
||||||||
| Pricing: |
|
||||||||
| Chemical Purity: | 96% | ||||||||
| Molecular Weight: | 118.13 | ||||||||
| Structure: |
|
||||||||
| Category: | Reference Standards for Inborn Errors | ||||||||
| Literature References: |
Mock, D.M., Henrich, C.L., Carnell, N., Mock, N.I., Indicators of marginal biotin deficiency and repletion in humans: validation of 3-hydroxyisovaleric acid excretion and a leucine challenge. Am J Clin Nutr, 2002, 76(5):1061-1068. |
||||||||
| MSDS: | |||||||||
| Applications: | Metabolite of leucine excreted in the urine. Elevated levels are a marker for Dihydrolipoamide dehydrogenase deficiency among other disorders. Also elevated levels are seen in smokers. |