Product: 3-Hydroxytetradecanedioic acid
Catalog Number: 5196
CAS Number: 73179-89-2
Pricing:
1 mg =  $390   Add to Cart
5 mg =  $1,250   Add to Cart
Molecular Weight: 274.35
Structure: 3-Hydroxytetradecanedioic acid
Category: Reference Standards for Inborn Errors
Literature References:

Bennett, M.J., Weinberger, M.J., Kobori, J.A., Rinaldo, P., Burlina, A.B., Mitochondrial Short-Chain L-3-Hydroxyacl-Coenzyme A Dehydrogenase Deficiency: A New Defect of Fatty Acid Oxidation. Pediatric Research, 1996, 39:185-188.

MSDS:
Applications: A metabolite of 3-hydroxydicarboxylic acid found in urine. High levels are detected in patients with 3-hydroxydicarboxylic aciduria. Occurs due to acute intoxication associated with hopantenate.