Product: | 3-Methylcrotonyl Glycine | ||||||||
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Catalog Number: | 5214 | ||||||||
CAS Number: | 33008-07-0 | ||||||||
Synonyms: | 3-Methyl Crotonyl Glycine | ||||||||
Pricing: |
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Formula: | C7H11NO3 | ||||||||
Molecular Weight: | 157.17 | ||||||||
Structure: | |||||||||
Appearance: | White solid | ||||||||
Category: | Reference Standards for Inborn Errors | ||||||||
Stability: | Stable under recommended storage conditions. | ||||||||
Storage: |
Material should be store in a tightly sealed container. Store at 4°C |
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Transportation: |
Non-hazardous for transport |
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Literature References: |
Arnold, G.L., et al., A Delphi-based consensus clinical practice protocol for the diagnosis and management of 3-methylcrotonyl CoA carboxylase deficiency. Molecular Genetics and Metabolism, 2008, 93(4):363-370. |
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MSDS: | |||||||||
Description: | An acyl glycine. A normal amino acid metabolite found in urine. Increased levels are found in patients with leucine catabolic disorders such as 3-methylcrotonyl-CoA carboxylase deficiency. A diagnostic marker for organic acidemias. |