Product: Succinylacetone-3,4,5,6,7-13C5
Catalog Number: C1282
CAS Number: 881835-86-5
Synonyms: Succinylacetone-13C5;
4,6-Dioxoheptanoic Acid-13C5;
NSC 174804-13C5
Pricing:
10 mg =  $1,290   (In Stock) Add to Cart
Formula: C213C5H10O4
Enrichment: 99%13C
Molecular Weight: 163.12
Structure: Succinylacetone-3,4,5,6,7-<sup>13</sup>C<sub>5</sub>
Appearance: White solid
Category: Research Compounds
Stability: Stable under recommended storage conditions
Storage:

Keep container tightly closed in a dry and well-ventilated place. Store at -20°C
Transportation:

Non-hazardous for transport
Literature References:

Kvittingen, E., et al.: Inher. Metab. Dis., 14, 554 (1991), Lindstedt, S., et al.: Lancet, 340, 813 (1992), Schulze, A., et al.: Clin. Chem., 47, 1424 (2001), Allard, P., et al.: Clin. Biochem., 37, 1010 (2004)
MSDS:
Description:

Succinylacetone (SA) is a specific marker for the inherited metabolic disease, hepatorenal tyrosinemia. It was developed a stable-isotope for the determination of SA in dried blood spots (DBS) and liquid urine using a 13C4-SA as internal standard. The method was applied retrospectively and prospectively for the diagnosis of hepatorenal tyrosinemia and for follow-up of patients under treatment.