Inquire About a Product| Product: | 3-Methylcrotonyl Glycine | ||||||||
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| Catalog Number: | 5214 | ||||||||
| CAS Number: | 33008-07-0 | ||||||||
| Synonyms: | 3-Methyl Crotonyl Glycine | ||||||||
| Pricing: |
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| Formula: | C7H11NO3 | ||||||||
| Molecular Weight: | 157.17 | ||||||||
| Structure: |
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| Appearance: | White solid | ||||||||
| Category: | Reference Standards for Inborn Errors | ||||||||
| Stability: | Stable under recommended storage conditions. | ||||||||
| Storage: |
Material should be store in a tightly sealed container. Store at 4°C |
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| Transportation: |
Non-hazardous for transport |
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| Literature References: |
Arnold, G.L., et al., A Delphi-based consensus clinical practice protocol for the diagnosis and management of 3-methylcrotonyl CoA carboxylase deficiency. Molecular Genetics and Metabolism, 2008, 93(4):363-370. |
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| MSDS: | |||||||||
| Description: | An acyl glycine. A normal amino acid metabolite found in urine. Increased levels are found in patients with leucine catabolic disorders such as 3-methylcrotonyl-CoA carboxylase deficiency. A diagnostic marker for organic acidemias. |