Product: | Succinylacetone-3,4,5,6,7-13C5 | ||||
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Catalog Number: | C1282 | ||||
CAS Number: | 881835-86-5 | ||||
Synonyms: |
Succinylacetone-13C5; 4,6-Dioxoheptanoic Acid-13C5; NSC 174804-13C5 |
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Pricing: |
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Formula: | C213C5H10O4 | ||||
Enrichment: | 99%13C | ||||
Molecular Weight: | 163.12 | ||||
Structure: | |||||
Appearance: | White solid | ||||
Category: | Research Compounds | ||||
Stability: | Stable under recommended storage conditions | ||||
Storage: |
Keep container tightly closed in a dry and well-ventilated place. Store at -20°C |
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Transportation: |
Non-hazardous for transport |
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Literature References: |
Kvittingen, E., et al.: Inher. Metab. Dis., 14, 554 (1991), Lindstedt, S., et al.: Lancet, 340, 813 (1992), Schulze, A., et al.: Clin. Chem., 47, 1424 (2001), Allard, P., et al.: Clin. Biochem., 37, 1010 (2004) |
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MSDS: | |||||
Description: |
Succinylacetone (SA) is a specific marker for the inherited metabolic disease, hepatorenal tyrosinemia. It was developed a stable-isotope for the determination of SA in dried blood spots (DBS) and liquid urine using a 13C4-SA as internal standard. The method was applied retrospectively and prospectively for the diagnosis of hepatorenal tyrosinemia and for follow-up of patients under treatment. |